Clinical Trials Directory

Trials / Conditions / Cystic Fibrosis

Cystic Fibrosis

1,360 registered clinical trials studyying Cystic Fibrosis81 currently recruiting.

StatusTrialSponsorPhase
Not Yet RecruitingPharmacokinetics of CFTR Modulators in Pregnant Individuals and in Postpartum Breastfeeding Mothers
NCT04940533
University of Minnesota
Not Yet RecruitingNovel Point-of-care Sweat Chloride Testing Device for Monitoring CFTR Function
NCT07414810
Emory UniversityN/A
Not Yet RecruitingTele-Rehabilitation in Adults With Cystic Fibrosis
NCT07500493
King Saud UniversityN/A
Not Yet RecruitingEffects of High-Frequency Chest Wall Oscillation Combined With Concurrent Training on Cough,in Cystic Fibrosis
NCT07519460
Riphah International UniversityN/A
Not Yet RecruitingSafety and Efficacy of Inhaled BMD003 (CFTR mRNA) in Chinese Cystic Fibrosis Patients Aged ≥12 Years
NCT07485543
Peking Union Medical College HospitalEARLY_Phase 1
RecruitingDose Escalation Study Evaluating the Safety and Pharmacokinetics of VX-272 in Healthy Participants
NCT07437105
Vertex Pharmaceuticals IncorporatedPhase 1
CompletedEffect of Vanzacaftor/Tezacaftor/Deutivacaftor (VNZ/TEZ/D-IVA) on the PK of Rosuvastatin in Healthy Participan
NCT07349394
Vertex Pharmaceuticals IncorporatedPhase 1
RecruitingDose Escalation Study Evaluating the Safety and Pharmacokinetics of VX-581 in Healthy Participants
NCT07283770
Vertex Pharmaceuticals IncorporatedPhase 1
RecruitingStudy of the Prevalence of Active/Passive Smoking and Vaping Among Patients With Cystic Fibrosis
NCT07342920
University Hospital, Strasbourg, France
RecruitingA Cohort for Inflammatory Respiratory Diseases: From Phenotyping to Personalised Medicine
NCT07274631
CHU de Reims
Not Yet RecruitingComparative Effects of Mechanical and Manual Airway Clearance Techniques in Cystic Fibrosis
NCT07062939
Riphah International UniversityN/A
WithdrawnRifaximin for Treatment of Bloating in Children and Adults With Cystic Fibrosis
NCT05408910
Wake Forest University Health SciencesPhase 2 / Phase 3
RecruitingAssessing Tenapanor as a Treatment of CF-related Constipation.
NCT06810167
Massachusetts General HospitalPhase 3
Active Not RecruitingA Long-term Study to Monitor the Health Status of People With Cystic Fibrosis Who Took Part in a Previous Stud
NCT06962852
Boehringer IngelheimPhase 1 / Phase 2
RecruitingRestarting Triple Therapy With Robust Monitoring for Adverse Events (RETRIAL)
NCT06683092
Boston Children's Hospital
RecruitingOral Health Status of Cystic Fibrosis Patients. An Online Survey in Collaboration With the Vaincre la Mucovisc
NCT06356246
Assistance Publique - Hôpitaux de Paris
CompletedA Phase 1 Study to Evaluate the Relative Bioavailability of a VX-828 Tablet Formulation
NCT06861413
Vertex Pharmaceuticals IncorporatedPhase 1
CompletedMuscle Endurance in Children With Cystic Fibrosis
NCT06812793
Bezmialem Vakif University
RecruitingRemote Sputum Collection in Cystic Fibrosis
NCT06950892
University of Pennsylvania
RecruitingContinuous Glucose Monitoring and OGTT Screen for Cystic Fibrosis Related Diabetes in Cystic Fibrosis
NCT06560463
Medical College of Wisconsin
RecruitingEvaluation of New Device for Beta-adrenergic Sweat Test in the Context of Stratification of Patient With Cysti
NCT06836453
Cliniques universitaires Saint-Luc- Université Catholique de LouvainN/A
RecruitingSafety, Tolerability and Efficacy Study of ARCT-032 in People With Cystic Fibrosis
NCT06747858
Arcturus Therapeutics, Inc.Phase 2
RecruitingStreamlined Treatment of Pulmonary Exacerbations in Pediatrics
NCT06654752
University of Washington, the Collaborative Health Studies Coordinating CenterN/A
RecruitingImpact of a Coordinated Dietetic-adapted Physical Activity Program on the Percentage of Lean Body Mass in Adul
NCT06457451
University Hospital, ToursN/A
Active Not RecruitingEvaluation of Long-term Safety and Efficacy of ELX/TEZ/IVA in Cystic Fibrosis Participants 12 Months of Age an
NCT06460506
Vertex Pharmaceuticals IncorporatedPhase 3
TerminatedA Study to Test How Well BI 3720931 is Tolerated and Whether it Improves Lung Function in People With Cystic F
NCT06515002
Boehringer IngelheimPhase 1 / Phase 2
RecruitingDevelopment of Non-Invasive Prenatal Diagnosis for Single Gene Disorders
NCT06147414
Assistance Publique - Hôpitaux de Paris
CompletedA Study to Investigate the Safety and Tolerability of Single and Multiple Ascending Doses of KIT2014 in Health
NCT06659757
Kither Biotech SrlPhase 1
Recruitinge-Health Program to Prevent Exacerbations in the Cystic Fibrosis Population
NCT06313827
University of ValenciaN/A
CompletedPerformances and Safety of MuCopilot, a Digital Tool for the Unsupervised Objective Assessment of Cystic Fibro
NCT06147778
Ad scientiamN/A
RecruitingA Research Study to Advance the CF Therapeutics Pipeline for People Without Modulators
NCT06504589
Nicole Hamblett
RecruitingPhysical Activity Profile and Sedentary Behaviour in Adults With Cystic Fibrosis
NCT06507956
Hospices Civils de Lyon
RecruitingA Phase 1/2 Trial of SP-101 for the Treatment of Cystic Fibrosis (CF)
NCT06526923
Spirovant Sciences, Inc.Phase 1 / Phase 2
RecruitingEstablishment of a Primary Epididymal Cell Model From Epididymal Samples to Study CFTR Gene Regulation
NCT06045702
University Hospital, Brest
RecruitingAcoustic Waveform Respiratory Evaluation
NCT06512064
Indiana UniversityN/A
TerminatedFrequency-time Analysis of Pathological Lung Sounds: Detection and Quantification of Pathological Sounds in Pa
NCT06399094
Groupe Hospitalier de la Region de Mulhouse et Sud Alsace
CompletedNatural History Study of Exocrine Pancreatic Function in Infants With Cystic Fibrosis (CF)
NCT06506773
Vertex Pharmaceuticals Incorporated
RecruitingA Usability Validation of the MuCopilot Mobile Application, a Digital Tool for the Unsupervised Objective Asse
NCT06132048
Ad scientiamN/A
Not Yet RecruitingMaralixibat in Patients With Cystic Fibrosis and Constipation, A Within-Subjects Pilot Study
NCT06413368
Children's Hospital Los AngelesPhase 2 / Phase 3
RecruitingSkin-interfaced Colorimetric Bifluidic Sweat Sensor Device for the Diagnosis of Cystic Fibrosis (CF)
NCT05998629
Milton S. Hershey Medical CenterN/A
CompletedA Two-Part Study to Evaluate the Efficacy, Safety, Tolerability and Pharmacokinetics of Repeat Doses of Inhale
NCT06478706
Enterprise Therapeutics LtdPhase 2
RecruitingSafety, Tolerability, Pharmacokinetics, and Preliminary Efficacy of SPL84 in Patients with Cystic Fibrosis
NCT06429176
SpliSense Ltd.Phase 2
CompletedA Study To Evaluate The Safety Of CMTX-101 In People With Cystic Fibrosis
NCT06159725
Clarametyx Biosciences, Inc.Phase 1 / Phase 2
RecruitingFLOWER: Following Longitudinal Outcomes With Epidemiology for Rare Diseases
NCT06539169
xCures
RecruitingTargeting Inflammation With Losartan to Improve Response to Modulator Therapy in Cystic Fibrosis.
NCT06364176
University of Kansas Medical CenterPhase 2
CompletedClinical Trial to Evaluate the Efficacy and Safety of Dirocaftor/Posenacaftor/Nesolicaftor in Adults With CF
NCT06468527
Kors van der EntPhase 2
CompletedIntrapulmonary Percussive Ventilation for Sputum Induction in Adults With Cystic Fibrosis
NCT06311292
Daniel J. WeinerN/A
RecruitingHealth Outcomes of Parents With Cystic Fibrosis-Aim 2
NCT06296394
University of Pittsburgh
RecruitingCircadian Rhythm Disorders in Children With Cystic Fibrosis Under CFTR (Cystic Fibrosis Transmembrane Conducta
NCT06370962
Hospices Civils de Lyon
Active Not RecruitingYOGA-CF (Yoga Outcomes Get Assessed in Cystic Fibrosis)
NCT06120465
Royal Brompton & Harefield NHS Foundation TrustN/A
CompletedEffect of One Year Elexacaftor-tezacaftor-ivacaftor Treatment
NCT06331000
University Hospital, Strasbourg, France
CompletedA Study to Test How Well BI 1291583 is Tolerated by People With Cystic Fibrosis Bronchiectasis (Clairafly™)
NCT05865886
Boehringer IngelheimPhase 2
CompletedA Study to Evaluate the Relative Bioavailability and Food Effect of a VX-118 Tablet Formulation
NCT06312787
Vertex Pharmaceuticals IncorporatedPhase 1
CompletedAn Intervention-Based Approach to Strengthen the Psychological Health of Children With Cystic Fibrosis and The
NCT06280066
Kirsehir Ahi Evran UniversitesiN/A
RecruitingSkeletal Health and Bone Marrow Composition in Adolescents With Cystic Fibrosis
NCT06216704
Massachusetts General Hospital
RecruitingFrench Validation of the AdT-Physio Scale
NCT06273566
Pole Sante Grace de Dieu
RecruitingImproving the Well-being of Caregivers of Cystic Fibrosis Patients During Physiotherapy Treatment
NCT06327802
Pole Sante Grace de Dieu
CompletedA Study of Vanzacaftor/Tezacaftor/Deutivacaftor (VNZ/TEZ/D-IVA) in Healthy Adult Panelists
NCT06299696
Vertex Pharmaceuticals IncorporatedPhase 1
RecruitingA Pilot and Feasibility Study to Evaluate High vs Low Glycemic Index Mixed Meal Tolerance Test in Adolescents
NCT06350149
Emory UniversityN/A
RecruitingCFTR Modulators in Pregnancy and Postpartum
NCT06302270
Region Stockholm
CompletedA Study To Evaluate the Relative Bioavailability, Food Effect, and Dose Proportionality of a Granule Formulati
NCT06299709
Vertex Pharmaceuticals IncorporatedPhase 1
RecruitingPathogenicity of Species of the Achromobacter Genus in Patients From Reunion Island With Cystic Fibrosis
NCT06371261
Centre Hospitalier Universitaire de la Réunion
UnknownExercise in People With Cystic Fibrosis on CFTR Modulator Therapy
NCT06322446
Universidad Politecnica de MadridN/A
CompletedDevelopment,Validity and Reliability of a Caregiver Version of the Breathlessness Beliefs Questionnaire
NCT06289972
Halic University
RecruitingMuscle Function and Physical Activity in the Modern Era of Cystic Fibrosis
NCT06251622
Hospices Civils de Lyon
CompletedEffect of Parental Attitude on Functional and Physical Level of Children With Cystic Fibrosis
NCT06306508
Halic University
Enrolling By InvitationMycobacteriophage Treatment of Non-tuberculosis Mycobacteria
NCT06262282
National Jewish Health
RecruitingA Phase 2 Study Evaluating Safety and Tolerability of RCT2100 (CFTR mRNA) in Healthy Participants and in Parti
NCT06237335
ReCode TherapeuticsPhase 2
Active Not RecruitingSGLT2 Inhibitor Therapy in Cystic Fibrosis-related Diabetes
NCT06149793
University of MinnesotaPhase 2 / Phase 3
RecruitingRegional Monitoring of CF Lung Disease
NCT06339593
Children's Hospital Medical Center, CincinnatiEARLY_Phase 1
CompletedDevelopment a Core Set for Adults With Cystic Fibrosis Based on the ICF
NCT06128499
Hacettepe University
RecruitingEvaluation of VX-828 in Healthy Participants and in Participants With Cystic Fibrosis
NCT06154447
Vertex Pharmaceuticals IncorporatedPhase 1
RecruitingImpact of Highly Effective Modulator Therapy on the Cystic Fibrosis Microbiome
NCT05982795
Dartmouth-Hitchcock Medical Center
UnknownDynamic Chest X-ray With Simultaneous Spirometry
NCT06122051
Liverpool Heart and Chest Hospital NHS Foundation Trust
CompletedSemaglutide in CFRD
NCT05788965
University of MinnesotaPhase 2 / Phase 3
Not Yet RecruitingENHANCE- Establishing Natural History in an Advanced New CF Care Era
NCT05986045
Royal College of Surgeons, Ireland
UnknownMultispectral Optoacoustic Tomography in Patients With Cystic Fibrosis
NCT06063785
University of Erlangen-Nürnberg Medical School
UnknownCeftolozane/Tazobactam Continuous Infusion for Infective Exacerbations of Cystic Fibrosis and Bronchiectasis
NCT06035055
Sunshine Coast Hospital and Health ServicePhase 4
RecruitingLung Transplant READY CF 2: CARING CF Ancillary RCT
NCT06032273
University of WashingtonN/A
Active Not RecruitingLung Transplant READY CF 2: A Multi-site RCT
NCT06030206
University of WashingtonN/A
CompletedThe Development and Evaluation of iCF-PWR for Healthy Siblings of Individuals With Cystic Fibrosis
NCT06012084
University of ReginaN/A
UnknownThe Effect of Bone Mineral Density in Patients With Adult Cystic Fibrosis
NCT06088485
Hacettepe University
TerminatedSymptom Based Performance of Airway Clearance After Starting Highly Effective Modulators for Cystic Fibrosis (
NCT05392855
University of Missouri-ColumbiaN/A
RecruitingThe Effects of a Low Glycemic Load Diet on Dysglycemia and Body Composition in Adults With Cystic Fibrosis-Rel
NCT05723445
Rhode Island HospitalN/A
RecruitingCF Organization of Care in the Era of Highly Effective Modulator.
NCT06599892
Hospices Civils de Lyon
Not Yet RecruitingPeer-supporting for Teenagers With Cystic Fibrosis in the Transition of Care From Paediatric to Adult Services
NCT05795673
Hospices Civils de LyonN/A
UnknownRelationship Between Health Literacy and Physical Activity in Adult Patients With Cystic Fibrosis
NCT05963503
Hacettepe University
Enrolling By InvitationEvaluation of Long-Term Safety and Efficacy of Vanzacaftor/Tezacaftor/Deutivacaftor in Cystic Fibrosis Partici
NCT05844449
Vertex Pharmaceuticals IncorporatedPhase 3
UnknownEvolution of the 6-minute Walk Test in Patients Treated With ELEXACAFTOR / TEZACAFTOR / IVACAFTOR
NCT06184763
Hospices Civils de Lyon
UnknownCystic Fibrosis and Periodontal Diseases
NCT06133335
CHU de ReimsN/A
CompletedAlternate Measures of Glucose During OGTT Testing for CFRD
NCT05568134
Children's Hospital of Philadelphia
CompletedHealth Outcomes of Parents With Cystic Fibrosis
NCT05829694
University of Pittsburgh
CompletedANNE Sensor Monitoring in Cystic Fibrosis
NCT05941832
Papworth Hospital NHS Foundation Trust
RecruitingA Study Assessing KB407 for the Treatment of Cystic Fibrosis
NCT05504837
Krystal Biotech, Inc.Phase 1
RecruitingFEED-Cystic Fibrosis (FEED-CF)
NCT05766774
Emory UniversityN/A
UnknownThe Living With a Long-Term Condition Study
NCT06072287
King's College London
CompletedEvaluation of Elexacaftor/Tezacaftor/Ivacaftor (ELX/TEZ/IVA) in Cystic Fibrosis (CF) Participants 12 to Less T
NCT05882357
Vertex Pharmaceuticals IncorporatedPhase 3
UnknownUnderstanding Gut Symptoms in People With Cystic Fibrosis
NCT05934656
University of Nottingham
CompletedEffects of Telerehabilitation-based Exercises in Cystic Fibrosis
NCT05590169
Istanbul Bilgi UniversityN/A
UnknownEvaluating Bronchodilator Response in Patients With Bronchiectasis
NCT05932316
Rambam Health Care CampusN/A
RecruitingEstrogen Supplementation and Bone Health in Women With CF
NCT05704036
Johns Hopkins UniversityPhase 4
CompletedReproducibility of Virtual Exercise Assessments Versus Face-to-face Exercise Testing in Adults With Cystic Fib
NCT06565832
Royal Brompton & Harefield NHS Foundation TrustN/A
CompletedAn Electrocardiogram Study to Evaluate the Effect of Vanzacaftor on the QT/QTc Interval in Healthy Participant
NCT05867147
Vertex Pharmaceuticals IncorporatedPhase 1
RecruitingStandardizing Treatments for Pulmonary Exacerbations - Aminoglycoside Study
NCT05548283
Chris GossPhase 4
Active Not RecruitingStrength and Muscle Related Outcomes for Nutrition and Lung Function in CF
NCT05639556
Jaeb Center for Health Research
RecruitingSinus Disease in Young Children With Cystic Fibrosis
NCT06191640
University of California, Los Angeles
Active Not RecruitingA Study of the Clinical Benefit of Tobramycin Inhalation Solution
NCT06106789
Qianfoshan Hospital
TerminatedNeuromodulation for Children With Cystic Fibrosis Experiencing Chronic Abdominal Pain
NCT05515250
St. Louis UniversityN/A
RecruitingHormonal Responses to a Mixed Meal in People With Cystic Fibrosis
NCT06163482
University of CincinnatiEARLY_Phase 1
CompletedInhaled Mannitol on Mucociliary Clearance in Moderate to Severe Cystic Fibrosis
NCT05740618
University of North Carolina, Chapel HillPhase 4
RecruitingStudy to Assess Amphotericin B Cystetic for Inhalation (ABCI) Doses in Healthy Volunteers & People with Cystic
NCT05802264
Cystetic Medicines, Inc.Phase 1
UnknownSweat Response, Sweat Composition and Thermoregulatory Response to Exercise in Heat in Adults With Cystic Fibr
NCT05896488
University of Portsmouth
CompletedEvaluation of the Evolution of Quality of Life in Relation to Naso-sinus Symptomatology Under Treatment With C
NCT05581056
Hospices Civils de Lyon
UnknownEffectiveness of CFTR Modulators According to Co-therapy
NCT05663255
Hospices Civils de Lyon
RecruitingA Phase 1/2 Study of VX-522 in Participants With Cystic Fibrosis (CF)
NCT05668741
Vertex Pharmaceuticals IncorporatedPhase 1 / Phase 2
CompletedSafety, Tolerability, and Pharmacokinetics of ARCT-032 in Healthy Adult Subjects and Adults With Cystic Fibros
NCT05712538
Arcturus Therapeutics, Inc.Phase 1
WithdrawnStudy to Determine the Efficacy&Safety of ARV-1801(ACG-701) for the Treatment of Cystic Fibrosis Pulmonary Exa
NCT05641298
AceragenPhase 2
UnknownSimultaneous quanTification of Elexacaftor/tezAcaftor/Ivacaftor Via Reverse Phase High Performance liquiD chro
NCT05822102
National Jewish Health
UnknownVolatilomic Approaches for the Study of CFTR Modulators (VOLATIL-CF)
NCT05726994
Assistance Publique - Hôpitaux de Paris
CompletedSafety, Tolerability, and Pharmacokinetics of SPL84 in Healthy Volunteers
NCT06217952
SpliSense Ltd.Phase 1
UnknownPilot Trial of ExACT (Exercise as Airway Clearance Therapy) for People With Cystic Fibrosis
NCT05482048
University Hospital Southampton NHS Foundation TrustN/A
CompletedStudy to Assess an Enteric Microgranule Formulation of Adrulipase in Patients With Cystic Fibrosis
NCT05719311
Entero TherapeuticsPhase 2
Enrolling By InvitationBreath Analysis and Arterial Stiffness in Patients With Respiratory Diseases
NCT05727852
I.M. Sechenov First Moscow State Medical University
UnknownFunctional Tests to Resolve Unsolved Rare Diseases. Rares.
NCT05696912
University Hospital, BordeauxN/A
CompletedCOVID-19 ANtibody Responses in Cystic Fibrosis: CAR-CF
NCT05745948
Hospital Universitari Vall d'Hebron Research Institute
UnknownFitness, Body Composition, Physical Activity and Sleep Patterns in People With Cystic Fibrosis on Modulator Th
NCT05857709
University of Portsmouth
TerminatedImipenem/Cilastatin/Relebactam Pharmacokinetics, Safety, and Outcomes in Adults and Adolescents With Cystic Fi
NCT05561764
Hartford HospitalPhase 4
UnknownCombating Diagnostic Wandering and Impasse for Cystic Fibrosis
NCT05654480
Societe Francaise de la Mucoviscidose
UnknownUse of A-STEP Test in Cystic Fibrosis Patients
NCT05809492
Marmara UniversityN/A
Active Not RecruitingCardiac Structure and Function in Patients with Cystic Fibrosis
NCT06084468
Herlev and Gentofte Hospital
UnknownThe Relationship Between Diet and Glycemic Response and Inflammatory Markers in Children With Cystic Fibrosis
NCT05748444
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Enrolling By InvitationProspective Healthcare-Associated Links in Transmission of Nontuberculous Mycobacteria
NCT05686837
University of North Carolina, Chapel Hill
CompletedAssessment of Cognitive Function and Exercise Capacity in Cystic Fibrosis
NCT06175182
Hacettepe University
CompletedObservational Study Comparing Home to Office Spirometry
NCT05285410
Chris Goss
Active Not RecruitingStudy to Evaluate Elexacaftor/Tezacaftor/Ivacaftor (ELX/TEZ/IVA) Long-term Safety and Efficacy in Subjects Wit
NCT05331183
Vertex Pharmaceuticals IncorporatedPhase 3
Active Not RecruitingA Study Evaluating the Long-term Safety and Efficacy of VX-121 Combination Therapy
NCT05444257
Vertex Pharmaceuticals IncorporatedPhase 3
CompletedEffectiveness of Respiratory Physiotherapy on Frequency of Exacerbations, Lung Function and Quality of Life Af
NCT07088614
University of AmericasN/A
CompletedClinical and Genetic Profile of Pediatric Patients With Cystic Fibrosis in Sohag.
NCT05599958
Sohag University
CompletedA Phase 1b/2 Trial of the Safety and Microbiological Activity of Bacteriophage Therapy in Cystic Fibrosis Subj
NCT05453578
National Institute of Allergy and Infectious Diseases (NIAID)Phase 1 / Phase 2
Active Not RecruitingDeterminants of Daily Physical Activity Level in Patients With Cystic Fibrosis - Pilot Study Protocol
NCT05206097
University Hospital, LimogesN/A
CompletedA Study to Evaluate the Relative Bioavailability of a Fixed-dose Combination Tablet of VX-121/Tezacaftor/Deuti
NCT05535959
Vertex Pharmaceuticals IncorporatedPhase 1
Active Not RecruitingColorectal Cancer Screening in Cystic Fibrosis
NCT05362344
University of Washington, the Collaborative Health Studies Coordinating Center
CompletedBaby Detect : Genomic Newborn Screening
NCT05687474
Centre Hospitalier Universitaire de Liege
UnknownReal-world Efficacy and Safety of Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulator Therapy
NCT05526027
Universitair Ziekenhuis BrusselN/A
UnknownDaily Monitoring of Respiratory Symptoms and Spirometry During ETI Treatment in Persons With Cystic Fibrosis.
NCT05599230
CHC Montlegia
UnknownCOVID-19 Antibody Responses in Cystic Fibrosis
NCT05561868
Children's Health Ireland
RecruitingCOVID-19 Antibody Responses In Cystic Fibrosis
NCT06274840
Pilar Azevedo
WithdrawnThe Relationship Between CFTR Gene Mutations and Exercise Capacity
NCT05157646
Virginia Commonwealth UniversityN/A
CompletedReal-Time Assessment of Lung Structure and Function in Children and Young Adults With CF Using Electrical Impe
NCT05455671
University of Colorado, Denver
CompletedPilot Study to Evaluate a Voice Journaling Application in Adolescents With Cystic Fibrosis
NCT05420844
University of Colorado, DenverN/A
CompletedInhaled Therapy Adherence and Outcomes to Kaftrio in Cystic Fibrosis
NCT05519020
Sheffield Teaching Hospitals NHS Foundation Trust
CompletedPharmacokinetics and Safety Assessment of VX-121/Tezacaftor/Deutivacaftor in Participants With Moderate Hepati
NCT05437120
Vertex Pharmaceuticals IncorporatedPhase 1
CompletedVideo Telehealth Exercise Training in Cystic Fibrosis
NCT04680403
University of Alabama at BirminghamN/A
CompletedEfficacy of Intensive Cholecalciferol Monitoring and Supplementation on Serum vitD Levels in Pediatric Patient
NCT05276960
Hospital Infantil de Mexico Federico GomezPhase 4
RecruitingEvaluation of VX-121/Tezacaftor/Deutivacaftor in Cystic Fibrosis (CF) Participants 1 Through 11 Years of Age
NCT05422222
Vertex Pharmaceuticals IncorporatedPhase 3
CompletedNebulized Bacteriophage Therapy in Cystic Fibrosis Patients With Chronic Pseudomonas Aeruginosa Pulmonary Infe
NCT05010577
BiomX, Inc.Phase 1 / Phase 2
CompletedCOVID-19 Antibody Responses in Cystic Fibrosis
NCT05614336
Hospices Civils de LyonN/A
CompletedCefiderocol Pharmacokinetics in Adult Patients With Cystic Fibrosis
NCT05314764
Hartford HospitalPhase 4
CompletedEvaluation of Efficacy and Safety of Elexacaftor/Tezacaftor/Ivacaftor (ELX/TEZ/IVA) in Cystic Fibrosis Subject
NCT05274269
Vertex Pharmaceuticals IncorporatedPhase 3
RecruitingBEGIN Novel ImagiNG Biomarkers
NCT05517655
Children's Hospital Medical Center, CincinnatiPhase 4
CompletedCystic Fibrosis and Frailtyh What's in Common?
NCT06020547
Federico II University
CompletedInvestigation of Relationship Between Vascular Functions, Exercise Capacity, and Respiratory Functions in CF
NCT04259983
Hacettepe University
UnknownRole of Toilet Bronchoscopy in RICU
NCT04798118
Assiut UniversityN/A
UnknownRemote Monitoring of High-Risk Patients With Chronic Cardiopulmonary Diseases
NCT04825067
Institute of Bioengineering and Bioimaging (IBB)N/A
UnknownGut Imaging for Function and Transit in Cystic Fibrosis 3 Junior
NCT05699148
Nottingham University Hospitals NHS Trust
UnknownStudy of Satisfaction of Patients and Care Providers for an Alternate Follow-up With In-hospital Consults and
NCT05249322
Hospices Civils de LyonN/A
TerminatedValidation of Therapeutic Efficacy Targeting the Splicing Variants in Cystic Fibrosis and CFTR Pathologies
NCT05100823
University Hospital, MontpellierN/A
CompletedTAAI Erasmus Research Initiative to Fight CF: Monitoring Inflammation in CF Lung Disease Into a New Era
NCT05752019
Erasmus Medical Center
RecruitingPatienthèque of Finisterian (South of Brittany) Children With Cystic Fibrosis in the Time of Precision Medicin
NCT04137133
University Hospital, BrestN/A
CompletedFeasibility of Home-based Exercise Program for Adults With Cystic Fibrosis
NCT05239611
University of Kansas Medical CenterPhase 2
UnknownDescription of the Short-term Effects of KAFTRIO® by Continuous Monitoring With the PHEAL-CR-K Application in
NCT05295524
Hopital FochN/A
WithdrawnA Study of Inhaled KB407 for the Treatment of Cystic Fibrosis
NCT05095246
Krystal Biotech, Inc.Phase 1
CompletedPilot Study of a CF-specific CBT Intervention for Adolescents
NCT05271643
Massachusetts General HospitalN/A
CompletedStudy to Assess the Safety and PK of Oral and IV Xenleta in Adults With Cystic Fibrosis
NCT05225805
Nabriva Therapeutics AGPhase 1
CompletedA Comprehensive Approach To Relief Of Digestive Symptoms In Cystic Fibrosis: CARDS-CF
NCT05251467
Nottingham University Hospitals NHS Trust
UnknownTrikafta/Kaftrio and Pseudomonas Aeruginosa
NCT05675592
Ospedale San Raffaele
Active Not RecruitingEffect of Losartan in Cystic Fibrosis (CF)-NIH Grant #133240
NCT03435939
University of Kansas Medical CenterEARLY_Phase 1
Active Not RecruitingCOVID-19 Antibody Responses In Cystic Fibrosis
NCT05074680
Insel Gruppe AG, University Hospital Bern
RecruitingMetformin for People With CFRD on CFTR Modulator Therapy to Improve Ion Channel Function
NCT04530383
University of Kansas Medical CenterPhase 2
UnknownCOVID-19 Antibody Responses in Cystic Fibrosis (CAR-CF)
NCT05217784
Rabin Medical Center
CompletedPilocarpine Microneedles for Sweat Induction (PMN-SI)
NCT04732195
Emory UniversityN/A
CompletedPerceptions of the CF Screening Protocol Incorporating NGS
NCT06299566
King's College London
CompletedEvaluation of Long-term Safety and Efficacy of ELX/TEZ/IVA in Cystic Fibrosis (CF) Participants 2 Years and Ol
NCT05153317
Vertex Pharmaceuticals IncorporatedPhase 3
CompletedA Study Evaluating the Safety of Elexacaftor/Tezacaftor/Ivacaftor in Participants With Cystic Fibrosis (CF)
NCT05111145
Vertex Pharmaceuticals IncorporatedPhase 3
Active Not RecruitingAirway Microbiome of Cystic Fibrosis Patients
NCT06057558
University Hospital, AntwerpN/A
UnknownRenal Impact of KAFTRIO in Mucoviscidose Population
NCT06197490
Hospices Civils de Lyon
Active Not RecruitingPEP and O-PEP Device for Nebulization in Cystic Fibrosis
NCT06964074
National Institute for Tuberculosis and Lung Diseases, PolandN/A
UnknownCOVID-19 Antibody Responses In Cystic Fibrosis
NCT05158829
Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico
WithdrawnThermic Effect of Feeding in Cystic Fibrosis
NCT03931252
Virginia Commonwealth UniversityN/A
UnknownPerformance and Patient Acceptance of a Commercially Available Beverage as Compared to an Oral Glucose Solutio
NCT05377502
Academisch Medisch Centrum - Universiteit van Amsterdam (AMC-UvA)
CompletedLung Transplant READY Pilot Study
NCT05135156
University of WashingtonN/A
CompletedA Study to Assess the Safety, Tolerability, and Pharmacokinetics of Brensocatib Tablets in Adults With Cystic
NCT05090904
Insmed IncorporatedPhase 2
RecruitingIdentification of Dysglycemia With Continuous Glucose Monitoring to Assess Clinical Evolution in Cystic Fibros
NCT05099939
Institut de Recherches Cliniques de Montreal
CompletedPsychosocial Factors and Quality of Life in the Effect of Fear of COVID-19 With Cystic Fibrosis
NCT05195216
Elif Kabasakal
UnknownCOVID-19 Antibody Responses In Cystic Fibrosis
NCT04863573
Queen's University, Belfast
RecruitingTrikafta Exercise Study in Cystic Fibrosis
NCT05279040
University of British Columbia
RecruitingCanadian Observational Study Evaluating the Long-term IMPACT of Cystic Fibrosis Transmembrane Conductance Regu
NCT05200429
University of British Columbia
CompletedKetone Supplementation in Cystic Fibrosis
NCT04938726
University of Alabama at BirminghamN/A
TerminatedStudy of a Nebulised Nitric Oxide Generating Solution in Patients With Mycobacterium Abscessus
NCT05101915
Papworth Hospital NHS Foundation TrustPhase 2
CompletedA Study of VX-121 Combination Therapy in Participants With Cystic Fibrosis (CF) Who Are Homozygous for F508del
NCT05076149
Vertex Pharmaceuticals IncorporatedPhase 3
RecruitingTissue Repository Providing Annotated Biospecimens for Approved Investigator-directed Biomedical Research Init
NCT05635266
Sanguine Biosciences
CompletedRemotely Supervised Exercise for Adults With Cystic Fibrosis
NCT05173194
Universidad Europea de MadridN/A
CompletedA Pilot Study of a Low Glycemic Load Diet in Adults With Cystic Fibrosis
NCT04519853
Boston Children's HospitalN/A
CompletedNETwork of Linoleic Acid Supplementation in Cystic Fibrosis
NCT04531410
Karolinska InstitutetN/A
CompletedTreatment With Elexacaftor/Tezacaftor/Ivacaftor, in Patients With Cystic Fibrosis and Caloric Intake
NCT06072365
University Hospital, Toulouse
Enrolling By InvitationGlobal Utilization And Registry Database for Improved preservAtion of doNor LUNGs
NCT04930289
Paragonix Technologies
CompletedEffects of Training Intensity on Physical Fitness and Body Composition in Cystic Fibrosis
NCT05140967
University of KielN/A
CompletedStudy to Evaluate Symptoms of Exocrine Pancreatic Insufficiency in Adult Participants With Cystic Fibrosis or
NCT05069597
AbbViePhase 4
CompletedThe Use of Breath Volatile Organic Compounds in Early Detection of Acute Pulmonary Exacerbations in Cystic Fib
NCT05944367
Papworth Hospital NHS Foundation Trust
CompletedA Study to Evaluate ELX/TEZ/IVA on Cough and Physical Activity in Participants With Cystic Fibrosis (CF)
NCT04969224
Vertex Pharmaceuticals IncorporatedPhase 3
CompletedCFTR Modulators and Gastrointestinal Complications
NCT05253859
Nottingham University Hospitals NHS Trust
Active Not RecruitingProspective Study of Pregnancy in Women With Cystic Fibrosis
NCT04828382
Amalia Magaret
CompletedA Phase 3 Study of VX-121 Combination Therapy in Participants With Cystic Fibrosis (CF) Heterozygous for F508d
NCT05033080
Vertex Pharmaceuticals IncorporatedPhase 3
UnknownIntestine-lung Axis of Cystic Fibrosis Patients Treated With the Combination Elexacaftor/Tezacaftor/Ivacaftor
NCT05937815
University Hospital, BordeauxN/A
Active Not RecruitingCOVID-19 Antibody Responses in Cystic Fibrosis
NCT05052294
University Hospital, Motol
TerminatedBright Light Therapy for Depression Symptoms in Adults With Cystic Fibrosis (CF) and COPD
NCT04921332
Erica OsbornN/A
RecruitingMarkers of Osteoporosis in Cystic Fibrosis
NCT03921060
University of Texas Southwestern Medical CenterPhase 4
CompletedSafety and Feasibility of High-intensity Interval Training Program in CF Patients
NCT04888767
Fondation IldysN/A
TerminatedCystic Fibrosis and Urinary Incontinence
NCT04922255
Megan BradleyN/A
WithdrawnA Dose-finding Study of Inhaled OligoG vs Placebo in Patients With Cystic Fibrosis
NCT03698448
AlgiPharma ASPhase 2 / Phase 3
CompletedCOVID-19 Antibody Responses In Cystic Fibrosis: CAR-CF
NCT05054582
Medical University Innsbruck
UnknownTraining in Shared Decision-making of Cystic Fibrosis Centers Competences in the Treatment of CF Related Diabe
NCT04891159
Hospices Civils de Lyon
CompletedCOVID-19 Antibody Responses in Cystic Fibrosis
NCT04992234
Vastra Gotaland Region
CompletedMagnetic Resonance Imaging and Neuro-Psychological Testing In Cystic Fibrosis
NCT04451213
Cardiff and Vale University Health BoardN/A
CompletedComparison Between Ultra-low-dose Computed Tomography and Lung MRI in Cystic Fibrosis
NCT04644471
Assistance Publique - Hôpitaux de ParisN/A
TerminatedCell Content of Sputum Induced by Hypertonic Saline in Adolescents With Cystic Fibrosis
NCT06909903
Assistance Publique Hopitaux De MarseilleN/A
RecruitingGLP-1 Agonist Therapy in Cystic Fibrosis-Related Glucose Intolerance
NCT04731272
University of PennsylvaniaPhase 2
UnknownOvarian Reserve in Women With Cystic Fibrosis and the Correlation With Demographic and Clinical Parameters
NCT05029817
Hadassah Medical Organization
CompletedClinical Effort Against Smoke Exposure in Cystic Fibrosis
NCT04777344
University of Alabama at BirminghamN/A
CompletedCystic Fibrosis Blood Neutrophils
NCT04970225
Assistance Publique - Hôpitaux de ParisN/A
CompletedMyVoice:CF Decision Aid for Women With Cystic Fibrosis
NCT04825236
University of PittsburghN/A
CompletedPharmacokinetics of Omadacycline in Cystic Fibrosis
NCT04460586
Paul BeringerPhase 4
CompletedIntegrating Electronic Patient Reported Biometric Measures (ePReBMs) From Wearable Devices in Respiratory Dise
NCT04857814
University of AlbertaN/A
CompletedA Decentralized Study to Evaluate Physical Activity and Cough Frequency Using Wearable Technology in Cystic Fi
NCT04923464
Vertex Pharmaceuticals Incorporated
CompletedPragmatic Implementation Trial of a CF Primary Palliative Care Intervention
NCT04923880
Massachusetts General HospitalN/A
Active Not RecruitingThe PROMISE Pediatric Study 6 to 11 Years Old
NCT04613128
Nicole Hamblett
CompletedA First in Human Study to Evaluate the Safety, Tolerability and Pharmacokinetics of Single and Multiple Ascend
NCT04926701
Enterprise Therapeutics LtdPhase 1
UnknownMonocytes as Predictors of Cystic Fibrosis-related Bone Disease
NCT04877223
Université de Reims Champagne-Ardenne
CompletedMENstrual Symptom Tracking to Understand and Assess (Women) Living With Cystic Fibrosis
NCT04620096
University of Washington
UnknownGeneral Health, Attitudes, and Activity in Self-directed Exercise in Patients With Cystic Fibrosis (GAINS-CF)
NCT04882267
University of VirginiaN/A
UnknownCovid-19 Antibody Responses in Cystic Fibrosis
NCT05012306
Universitätsklinikum Köln
CompletedHERO-2: Home-Reported Outcomes With CFTR Modulator Therapy
NCT04798014
Indiana University
CompletedCOVID-19 Antibody Responses In Cystic Fibrosis
NCT04904445
Erasmus Medical Center
CompletedCase-control Study of Sleep Disorders in Children With Cystic Fibrosis
NCT04847882
University Hospital, Strasbourg, France
TerminatedAirway Clearance for Pediatric and Adult Cystic Fibrosis Patients Using a Portable Intra-Pulmonary Percussion
NCT04743206
University of FloridaN/A
UnknownUse of Capnography for the Follow-up of Cystic Fibrosis Children
NCT04814797
Central Hospital, Nancy, France
RecruitingTesting Drug Efficacy in Cystic Fibrosis Through N-of-1 Trials
NCT04580368
Children's Hospital Medical Center, CincinnatiN/A
CompletedAcceptability, Feasibility and Preliminary Efficacy of CFWP to Treat Clinically Elevated Fatigue in Adults Wit
NCT04809207
Johns Hopkins UniversityN/A
CompletedBacille Calmette-Guerin (BCG) Vaccine for Immune Protection Against Infections
NCT04884308
Johns Hopkins UniversityPhase 2
UnknownA New Posaconazole Dosing Regimen for Paediatric Patients With Cystic Fibrosis and Aspergillus Infection
NCT04966234
Bambino Gesù Hospital and Research InstitutePhase 2 / Phase 3
CompletedThe Impact Of A Tele-Exercise Program For Children With Cystic Fibrosis During The Covid-19 Pandemic On Qualit
NCT05481190
Ondokuz Mayıs UniversityN/A
CompletedAn Assistive Powered Wheelchair: Stage 2 Trial
NCT05292690
East Kent Hospitals University NHS Foundation Trust
CompletedCYstic Fibrosis bacterioPHage Study at Yale (CYPHY)
NCT04684641
Yale UniversityPhase 1 / Phase 2
CompletedUpper Extremity Exercise Capacity, Muscle Oxygenation, Balance in Patients With Cystic Fibrosis
NCT04803643
Gazi University
CompletedOral Glucose Tolerance Testing Using Candy for Cystic Fibrosis
NCT04579939
Mayo ClinicN/A
CompletedConcerns of Children Whose Parents Have Cystic Fibrosis
NCT04702386
Assistance Publique - Hôpitaux de Paris
CompletedImmune Profiles in CF Fungal Infection
NCT04476758
University of Alabama at Birmingham
RecruitingRegional Phenotyping of CF and Non-CF Bronchiectasis
NCT04793867
Children's Hospital Medical Center, Cincinnati
WithdrawnCFTR Related Pancreatitis Study
NCT04274413
The Hospital for Sick ChildrenN/A
RecruitingQuantitation and Spatial Registration of Airways Dysfunction With Dynamic 19F MRI in Cystic Fibrosis
NCT06057714
University of North Carolina, Chapel Hill
CompletedEfficacy of an Infrared Visualization Technique for the Identification of the Peripheral Venous Access Site in
NCT04226118
Hospices Civils de LyonN/A
UnknownImproving Therapeutic Adherence With a Co-constructed Program Involving Both Patients and Health Care Professi
NCT03226795
Hospices Civils de LyonN/A
CompletedA Study to Assess the Effect of ELX/TEZ/IVA on Glucose Tolerance in Participants With Cystic Fibrosis (CF)
NCT04599465
Vertex Pharmaceuticals IncorporatedPhase 3
CompletedThe Impact of Patch Rx Technologies on Adherence to Vitamin and Trikafta Therapies in Patients With Cystic Fib
NCT04684823
The University of Texas Health Science Center at San AntonioN/A
CompletedFeasibility of a Goal-based Agenda Setting Intervention
NCT04696484
Dartmouth-Hitchcock Medical CenterN/A
CompletedA Study Evaluating the Long-term Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor in Cystic Fibrosis (C
NCT04545515
Vertex Pharmaceuticals IncorporatedPhase 3
CompletedSELF-BREATHE RCT for Chronic Breathlessness
NCT04574050
King's College Hospital NHS TrustN/A
CompletedPhysical Activity, Exercise Capacity and Coronavirus Phobia of Adult Cystic Fibrosis Patients During COVID-19
NCT04673331
Hacettepe University
WithdrawnMedication Adherence and Non-adherence in Adults With Rare Disease
NCT04541875
Xperiome
UnknownEffects of a Telerehabilitation Approach in Children With Cystic Fibrosis
NCT04683809
Marmara UniversityN/A
UnknownCharacterization of Pulmonary Microbiome in Cystic Fibrosis Patients
NCT04735679
University Hospital, Montpellier
UnknownEffect of the CFTR-modulating Triple Therapy Elexacaftor - Tezacaftor - Ivacaftor
NCT05576324
University of Erlangen-Nürnberg Medical School
CompletedThe Effects of Telerehabilitation on Muscle Function, Physical Activity and Sleep in Cystic Fibrosis During Pa
NCT04742049
Hacettepe UniversityN/A
CompletedQualitative Understanding of Experiences With the SIMPLIFY Trial
NCT04320381
Boston Children's Hospital
CompletedPh 1/2 Study Evaluating Safety and Tolerability of Inhaled AP-PA02 in Subjects With Chronic Pseudomonas Aerugi
NCT04596319
Armata Pharmaceuticals, Inc.Phase 1 / Phase 2
CompletedEvaluation of Lung T1-MRI in Pediatric Cystic Fibrosis Patients
NCT04994301
University Hospitals Cleveland Medical Center
Enrolling By InvitationProspective Analysis of Urine LAM to Eliminate NTM Sputum Screening
NCT04579211
Jerry A. Nick, M.D.
CompletedA Pilot Study to Assess the Effect of Intermittent iNO on the Treatment of NTM Lung Infection in CF and Non-CF
NCT04685720
Beyond Air Inc.N/A
WithdrawnEpidemiology and Treatment of Small-colony Variant Staphylococcus Aureus in Cystic Fibrosis
NCT02547116
Johns Hopkins UniversityPhase 4
WithdrawnHuman MesenchymAl Stem Cells Infusion in Patients With Cystic Fibrosis
NCT03058068
Joshua M HarePhase 1
CompletedFeasibility of a New Model for Exercise Prescription in Cystic Fibrosis
NCT04075864
University of Alabama at BirminghamN/A
CompletedEvaluation of ELX/TEZ/IVA in Cystic Fibrosis (CF) Subjects 2 Through 5 Years
NCT04537793
Vertex Pharmaceuticals IncorporatedPhase 3
RecruitingStudy to Evaluate Biological & Clinical Effects of Significantly Corrected CFTR Function in Infants & Young Ch
NCT04509050
Sonya Heltshe
Active Not RecruitingNon-contrast Lung Perfusion Mapping Applied for New Insights in Cystic Fibrosis
NCT04467957
Children's Hospital Medical Center, CincinnatiPhase 4
RecruitingExercise in Child Health
NCT05359991
University of California, IrvineN/A
CompletedStreamlined Treatment of Pulmonary Exacerbations in Pediatrics Pilot Study
NCT04608019
University of Washington, the Collaborative Health Studies Coordinating CenterN/A
TerminatedDeveloping Optimal Parameters for Hyperpolarized Noble Gas and Inert Fluorinated Gas MRI of Lung Disorders
NCT02748798
Thunder Bay Regional Health Research InstituteEARLY_Phase 1
RecruitingHyperpolarized 129Xe MR Imaging of Lung Function in Healthy Volunteers and Subjects With Pulmonary Disease
NCT04624490
Mario Castro, MD, MPHPhase 1
CompletedThe Effect of Telerehabilitation on Functional Capacity, Oxidative Stress and Respiratory Parameters in Cystic
NCT05147285
Hacettepe UniversityN/A
CompletedGut Imaging for Function & Transit in CF - GIFT-CF 3
NCT04618185
Nottingham University Hospitals NHS Trust
CompletedProximal Intestinal Obstruction Syndrome (PIOS) in a Patient With Cystic Fibrosis: A New Syndrome
NCT04613063
Tecnologico de Monterrey
CompletedManual Chest Physiotherapy and Active Cycle of Breathing Techniques (ACBT) in Patients of Cystic Fibrosis
NCT05026918
Riphah International UniversityN/A
Active Not RecruitingMicrobial Biomarkers of EArly Pseudomonas Aeruginosa Colonization in CHildren With Cystic Fibrosis
NCT03947957
University Hospital, BrestN/A
CompletedAssessment of Contraceptive Safety and Effectiveness in Cystic Fibrosis
NCT04568980
University of Washington
Active Not RecruitingReal World Clinical Outcomes With Novel Modulator Therapy Combinations in People With CF (RECOVER)
NCT04602468
Royal College of Surgeons, IrelandPhase 4
UnknownCystic Fibrosis Remote Monitoring System
NCT04453358
Koronis Biomedical TechnologiesN/A
CompletedImpact of Discontinuing Hypertonic Saline in People With CF on Highly Effective CFTR Modulators- A SIMPLIFY Su
NCT06350461
Nicole HamblettN/A
CompletedImpact of Discontinuing Dornase Alfa in People With CF on Highly Effective CFTR Modulator Therapy-A SIMPLIFY S
NCT06350474
Nicole HamblettN/A
CompletedImpact of Discontinuing Chronic Therapies in People With Cystic Fibrosis on Highly Effective CFTR Modulator Th
NCT04378153
Nicole Hamblett
WithdrawnVitamin K Supplementation to Reduce Deficiencies in Adults With Cystic Fibrosis
NCT04496921
Institut de Recherches Cliniques de MontrealN/A

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