| Not Yet Recruiting | Tolerability of Enteral NAC in Infants NCT06260566 | Sanjiv Harpavat | Phase 1 |
| Recruiting | The Use of Near-Infrared Fluorescence Cholangiography With Indocyanine Green (ICG) in the Work Up of Neonatal NCT07250854 | University of Alabama at Birmingham | EARLY_Phase 1 |
| Completed | Kasai Portoenterostomy Timing and Outcomes in Biliary Atresia NCT07328204 | The Children's Hospital of Zhejiang University School of Medicine | — |
| Not Yet Recruiting | Stool Card in Biliary Atresia NCT07139717 | Assiut University | — |
| Not Yet Recruiting | Clinical Outcomes of Early Kasai Surgery With Umbilical Cord MSCs in Biliary Atresia NCT07011199 | Universitas Diponegoro | Phase 1 |
| Recruiting | Nutritional Intervention for Biliary Atresia NCT06764082 | Tongji Hospital | N/A |
| Recruiting | Evaluation of the Use of Granulocyte Colony Stimulating Factor (GCSF) in Post Kasai Type 3 Biliary Atresia NCT06708572 | National Liver Institute, Egypt | N/A |
| Terminated | Study to Assess Efficacy, Safety, Tolerability, Pharmacokinetics (PK), and Pharmacodynamics (PD) of Obeticholi NCT06121375 | Intercept Pharmaceuticals | Phase 2 / Phase 3 |
| Recruiting | Use of Indocyanine Green (ICG) for the Diagnosis of Biliary Atresia NCT07513038 | Boston Children's Hospital | Phase 1 / Phase 2 |
| Unknown | Efficacy of New Post Kasai ILBS Protocol in Biliary Atresia. NCT06447051 | Institute of Liver and Biliary Sciences, India | — |
| Recruiting | Stem Cell Applications in Biliary Atresia Patients NCT06564740 | Necmi Kadıoğlu Hospital | N/A |
| Active Not Recruiting | Biliary Atresia Research Network Northeast NCT06184971 | Yale University | — |
| Unknown | Robot-assisted Modified Kasai Portoenterostomy Versus Open Kasai Portoenterostomy for Biliary Atresia NCT06219993 | Zunyi Medical College | — |
| Withdrawn | Intestinal Microbiome Composition in Infants With Biliary Atresia (BA) NCT03890536 | Children's Hospital Medical Center, Cincinnati | — |
| Recruiting | Preoperative Serum FGF19 in the Prognosis of Biliary Atresia NCT05848310 | Children's Hospital of Fudan University | — |
| Unknown | Part II: Granulocyte-Colony Stimulating Factor Adjunct Therapy for Biliary Atresia NCT04373941 | Holterman, Ai-Xuan, M.D. | Phase 2 |
| Recruiting | Preventive Effect of Prophylactic Oral Antibiotics Against Cholangitis After Kasai Portoenterostomy NCT05925309 | Children's Hospital of Fudan University | N/A |
| Unknown | Effect of Desflurane on Pediatric Acute Respiratory Distress Syndrome After Living Donor Liver Transplant Reci NCT05783518 | Tianjin First Central Hospital | Phase 4 |
| Completed | Norepinephrine for Prevention of Intraoperative Hypotension in Infants Undergoing Kasai Portoenterostomy NCT05521152 | Kasr El Aini Hospital | Phase 3 |
| Unknown | Definition for Biliary Atresia Associated Cholangitis After Surgery NCT05464303 | Nanjing Children's Hospital | — |
| Enrolling By Invitation | An Open-label Extension Study to Evaluate Long-term Efficacy and Safety of Odevixibat in Children With Biliary NCT05426733 | Albireo, an Ipsen Company | Phase 3 |
| Recruiting | High Medium-chain Triglyceride Nutritional Support in Infants With Biliary Atresia NCT05072626 | Children's Hospital of Fudan University | — |
| Completed | Evaluation of Maralixibat in Biliary Atresia Response Post-Kasai NCT04524390 | Mirum Pharmaceuticals, Inc. | Phase 2 |
| Completed | Investigation of Mortality, Morbidity and Risk Factors After Pediatric Liver Transplantation NCT04778735 | Memorial Bahçelievler Hospital | N/A |
| Recruiting | Molecular Characterization for Understanding Biliary Atresia NCT04272515 | Institut National de la Santé Et de la Recherche Médicale, France | N/A |
| Unknown | Predictive Models of Hepatic Decompensation and Survival Outcomes in Pediatric Patients With Cirrhosis NCT05181332 | West China Hospital | — |
| Unknown | A Real World Study on Clinical Efficacy of Bicarbonate Ringer's Solution in Biliary Atresia Children NCT04506021 | Tongji Hospital | — |
| Active Not Recruiting | Efficacy and Safety of Odevixibat in Children With Biliary Atresia Who Have Undergone a Kasai HPE (BOLD) NCT04336722 | Albireo, an Ipsen Company | Phase 3 |
| Recruiting | BILACO Trial: Biliary Atresia - a Severe Complex Congenital Liver Disease NCT05399745 | Rigshospitalet, Denmark | — |
| Unknown | Gut Microbiome in Biliary Atresia NCT04260503 | Yonsei University | — |
| Unknown | Dry Blood Spot Screening Test for Biliary Atresia（DBS-SCReBA） NCT03898765 | Xinhua Hospital, Shanghai Jiao Tong University School of Medicine | N/A |
| Completed | Outcome of Kasai Portoenterostomy in Biliary Atresia in Upper Egypt NCT05925543 | Aswan University Hospital | — |
| Unknown | Dry Blood Spot Screening Test for Neonatal Cholestasis Patients NCT03667534 | National Taiwan University Hospital | — |
| Completed | N-Acetylcysteine in Biliary Atresia After Kasai Portoenterostomy NCT03499249 | Baylor College of Medicine | Phase 2 |
| Completed | GCSF Adjunct Therapy for Biliary Atresia NCT03395028 | Holterman, Ai-Xuan, M.D. | EARLY_Phase 1 |
| Unknown | Early Predictors for the Short Term Native Liver Survival in Patients With Biliary Atresia After Kasai Procedu NCT05909033 | Weibing Tang | — |
| Completed | FibroScan™ in Pediatric Cholestatic Liver Disease (FORCE) NCT02922751 | Arbor Research Collaborative for Health | — |
| Completed | Ultrasound Shear Wave Elastography Evaluation of Suspected and Known Biliary Atresia NCT02652533 | Children's Hospital Medical Center, Cincinnati | — |
| Recruiting | Mapping Disease Pathways for Biliary Atresia NCT03273049 | University of Pittsburgh | — |
| Unknown | Clinical and Basic Study for Pediatric Liver Transplantation NCT02503384 | RenJi Hospital | — |
| Terminated | Obeticholic Acid in Pediatric Subjects With Biliary Atresia NCT05321524 | Intercept Pharmaceuticals | Phase 2 |
| Unknown | Peri Kasai Portoenterostomy Anchoring of the Jejunal Loop NCT04961034 | Tanta University | N/A |
| Completed | Autologous BMNC Infusion for Liver Cirrhosis in Children With BA NCT05517317 | Vinmec Research Institute of Stem Cell and Gene Technology | Phase 1 |
| Unknown | Development and Validation of a Screening Score for the Biliary Atresia in Infantile Cholestasis: A Prospectiv NCT03842150 | Xinhua Hospital, Shanghai Jiao Tong University School of Medicine | — |
| Completed | Safety Study of Intravenous Immunoglobulin (IVIG) Post-Portoenterostomy in Infants With Biliary Atresia NCT01854827 | National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK) | Phase 1 / Phase 2 |
| Terminated | Pentoxifylline Therapy in Biliary Atresia NCT01774487 | Baylor College of Medicine | Phase 2 |
| Unknown | Trail to Investigate the Effectiveness of CoSeal in Reducing Adhesions Following the Kasai Hepatoportoenterost NCT01745991 | Naved Alizai | — |
| Completed | Maternal Microchimerism in Lymph Nodes of Infants With Biliary Atresia at Time of Kasai's Operation NCT02292862 | Medizinische Hochschule Brandenburg Theodor Fontane | — |
| Completed | Biliary Atresia, Hepatic Buffer Response and Sevoflurane NCT02471209 | Children's Hospital of Fudan University | — |
| Completed | The Comparison of Desflurane and Sevoflurane on Postoperative Recovery and Hepatic Function of Biliary Atresia NCT01443572 | Yonsei University | N/A |
| Completed | Laparoscopic Kasai Has Similar Anesthetic Outcomes to Open Kasai NCT06163417 | Taichung Veterans General Hospital | — |
| Recruiting | Treating Primary Sclerosing Cholangitis and Biliary Atresia With Vancomycin NCT02137668 | Sacramento Pediatric Gastroenterology | Phase 1 |
| Recruiting | Rare Disease Patient Registry & Natural History Study - Coordination of Rare Diseases at Sanford NCT01793168 | Sanford Health | — |
| Completed | Gastrointestinal Microbiota in Primary Sclerosing Cholangitis and Biliary Atresia With Vancomycin NCT01322386 | Stanford University | Phase 1 |
| Recruiting | Biliary Atresia Study in Infants and Children NCT00345553 | Arbor Research Collaborative for Health | — |
| Completed | A Randomized, Double-Blinded, Placebo-Controlled Trial of Corticosteroid Therapy Following Portoenterostomy NCT00294684 | National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK) | N/A |
| Recruiting | A Prospective Database of Infants With Cholestasis NCT00061828 | Arbor Research Collaborative for Health | — |
| Unknown | Evaluation of Immune Function in Biliary Atresia Children With Prolonged Jaundice NCT00155194 | National Taiwan University Hospital | — |
| Completed | Use of Probiotics to Prevent Cholangitis in Children With Biliary Atresia After the Kasai Portoenterostomy NCT00166868 | National Taiwan University Hospital | N/A |
| Completed | Survival With Own Liver of Conventional Versus Laparoscopic Kasai for Biliary Atresia NCT01063699 | Hannover Medical School | N/A |
| Completed | Study of Magnesium Sulfate in Children With Reduced Bone Density Secondary to Chronic Cholestatic Liver Diseas NCT00007033 | National Center for Research Resources (NCRR) | N/A |
| Unknown | RCT of Steroids Following Kasai Portoenterostomy for Biliary Atresia. NCT00539565 | King's College Hospital NHS Trust | Phase 3 |