| Recruiting | Gene Modified Immune Cells After Conditioning Regimen for the Treatment of Stage IIIC or IV Melanoma or Metast NCT04119024 | Anusha Kalbasi | Phase 1 |
| Recruiting | Phase II Study of PD-1 Antibody Combined With Radiotherapy in Recurrent or Metastatic Adrenal Cortical Carcino NCT06587802 | Sun Yat-sen University | Phase 2 |
| Recruiting | Dostarlimab for Locally Advanced or Metastatic Cancer (Non-colorectal/Non-endometrial) With Tumor dMMR/MSI NCT06333314 | UNICANCER | Phase 2 |
| Recruiting | Study of Radiotherapy and Pembrolizumab in People With Adrenocortical Carcinoma NCT06066333 | Memorial Sloan Kettering Cancer Center | Phase 2 |
| Terminated | Phase 1 Study of 68Ga-R8760 NCT05999292 | Radionetics Oncology | Phase 1 |
| Recruiting | Surgical Treatment of Adrenal Diseases- Laparoscopic vs. Robotic-assisted Adrenalectomy NCT06050057 | University Hospital Olomouc | — |
| Unknown | The Adverse Event of Mitotane Therapy in Patients With Adrenocortical Carcinoma NCT05839886 | Shanghai Jiao Tong University School of Medicine | — |
| Terminated | A Phase II Study to Evaluate the Efficacy and Safety of Pembrolizumab in Combination With Mitotane in Patients NCT05634577 | M.D. Anderson Cancer Center | Phase 2 |
| Recruiting | Pembrolizumab in the Treatment of Advanced, Progressive Adrenocortical Carcinoma. NCT05563467 | Maria Sklodowska-Curie National Research Institute of Oncology | Phase 2 |
| Unknown | European Multicenter Study on Role of Lymph Node Dissection in Surgical Management of Adrenal Cortical Carcino NCT05763524 | Fondazione Policlinico Universitario Agostino Gemelli IRCCS | — |
| Unknown | Adrenal Vein Sampling as a Tool to Identify Biomarkers That Aid the Diagnosis of Adrenocortical Carcinoma NCT05660889 | Erasmus Medical Center | — |
| Recruiting | Evaluation of the Efficacy of Addition of Progesterone to Standard Chemotherapy in Adrenocortical Carcinoma (A NCT05913427 | Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia | Phase 2 |
| Completed | The Impact of Mitotane Therapy on Serum Free Proteins in Patients With Adrenocortical Carcinoma NCT05344027 | King's College Hospital NHS Trust | — |
| Active Not Recruiting | Phase II Trial of Pembrolizumab Plus Lenvatinib in Advanced Adrenal Cortical Carcinoma NCT05036434 | National Cancer Center, Korea | Phase 2 |
| Terminated | Milademetan in Advanced/Metastatic Solid Tumors NCT05012397 | Rain Oncology Inc | Phase 2 |
| Recruiting | Phase II Study for Combination of Camrelizumab and Apatinib in the Second-line Treatment of Recurrent or Metas NCT04318730 | West China Hospital | Phase 2 |
| Completed | Study of Relacorilant in Combination With Pembrolizumab for Patients With Adrenocortical Carcinoma Which Produ NCT04373265 | Corcept Therapeutics | Phase 1 |
| Terminated | A Novel Therapeutic Vaccine (EO2401) in Metastatic Adrenocortical Carcinoma, or Malignant Pheochromocytoma/Par NCT04187404 | Enterome | Phase 1 / Phase 2 |
| Terminated | Natural History Study of Children and Adults With Adrenocortical Cancer (ACC) NCT04447014 | National Cancer Institute (NCI) | — |
| Active Not Recruiting | Optimal Methods of Disease Progression and Survival Analysis in Children and Adults Patients With Adrenocortic NCT04358107 | National Cancer Institute (NCI) | — |
| Completed | First-in-human Evaluation of [18F]CETO NCT05361083 | Uppsala University | EARLY_Phase 1 |
| Unknown | Cabozantinib in Advanced Adrenocortical Carcinoma NCT03612232 | Wuerzburg University Hospital | Phase 2 |
| Terminated | A Phase 1 Study of [225Ac]-FPI-1434 Injection NCT03746431 | Fusion Pharmaceuticals Inc. | Phase 1 |
| Enrolling By Invitation | A Prospective Cohort Study for Patients With Adrenal Diseases NCT03474237 | Seoul National University Hospital | — |
| Completed | Adjuvant Chemotherapy vs. Observation/Mitotane After Primary Surgical Resection of Localized Adrenocortical Ca NCT03723941 | Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia | Phase 3 |
| Unknown | Cabazitaxel Activity in Patients With Advanced AdrenoCortical-Carcinoma Progressing After Previous Chemotherap NCT03257891 | Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia | Phase 2 |
| Active Not Recruiting | Nivolumab Combined With Ipilimumab for Patients With Advanced Rare Genitourinary Tumors NCT03333616 | Dana-Farber Cancer Institute | Phase 2 |
| Recruiting | Surgery and Heated Intraperitoneal Chemotherapy for Adrenocortical Carcinoma NCT03127774 | Columbia University | Phase 2 |
| Unknown | Activity of Abiraterone Acetate in the Management of Cushing's Syndrome in Patients With Adrenocortical Carcin NCT03145285 | Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia | Phase 2 |
| Recruiting | Familial Investigations of Childhood Cancer Predisposition NCT03050268 | St. Jude Children's Research Hospital | — |
| Active Not Recruiting | Single Agent Pembrolizumab in Subjects With Advanced Adrenocortical Carcinoma NCT02673333 | Memorial Sloan Kettering Cancer Center | Phase 2 |
| Completed | Structured Evaluation of adRENal Tumors Discovered Incidentally - Prospectively Investigating the Testing Yiel NCT02324647 | University Medical Center Groningen | — |
| Completed | Natural History and Tissue Acquisition Study of Adrenocortical Carcinoma NCT02015026 | National Cancer Institute (NCI) | — |
| Completed | Phase 1 Study of ATR-101 in Subjects With Advanced Adrenocortical Carcinoma NCT01898715 | Millendo Therapeutics, Inc. | Phase 1 |
| Completed | Surgery and Heated Chemotherapy for Adrenocortical Carcinoma NCT01833832 | National Cancer Institute (NCI) | Phase 2 |
| Terminated | Possible New Therapy for Advanced Cancer NCT01832974 | INSYS Therapeutics Inc | Phase 1 |
| Completed | Studying Genes in Samples From Younger Patients With Adrenocortical Tumor NCT01528956 | Children's Oncology Group | — |
| Completed | Clinical Trial of Dovitinib in First-line Metastatic or Locally Advanced Non-resectable Adrenocortical Carcino NCT01514526 | Spanish Oncology Genito-Urinary Group | Phase 2 |
| Completed | A Dose Finding Study of TKM-080301 Infusion in Neuroendocrine Tumors (NET) and Adrenocortical Carcinoma (ACC) NCT01262235 | Arbutus Biopharma Corporation | Phase 1 / Phase 2 |
| Completed | A Study of OSI-906 in Patients With Locally Advanced or Metastatic Adrenocortical Carcinoma NCT00924989 | Astellas Pharma Inc | Phase 3 |
| Completed | Seneca Valley Virus-001 and Cyclophosphamide in Treating Young Patients With Relapsed or Refractory Neuroblast NCT01048892 | Children's Oncology Group | Phase 1 |
| Unknown | Sorafenib Plus Paclitaxel in Adreno-Cortical-Cancer Patients NCT00786110 | University of Turin, Italy | Phase 2 |
| Unknown | Efficacy of Adjuvant Mitotane Treatment (ADIUVO) NCT00777244 | University of Turin, Italy | Phase 3 |
| Active Not Recruiting | Evaluation of Side Effects of Mitotane NCT00568139 | University of Wuerzburg | — |
| Completed | Sunitinib in Refractory Adrenocortical Carcinoma NCT00453895 | University of Wuerzburg | Phase 2 |
| Withdrawn | Treatment Study Using Bevacizumab for Patients With Adrenocortical Carcinoma NCT00469469 | Dartmouth-Hitchcock Medical Center | Phase 2 |
| Completed | Evaluation of 123I-Iodometomidate for Adrenal Scintigraphy NCT00454103 | University of Wuerzburg | Phase 1 / Phase 2 |
| Completed | Continuous Hyperthermic Peritoneal Perfusion (CHPP) With Cisplatin for Children With Peritoneal Cancer NCT00436657 | M.D. Anderson Cancer Center | Phase 1 |
| Completed | Tumor Necrosis Factor in Patients Undergoing Surgery for Primary Cancer or Metastatic Cancer NCT00436410 | National Institutes of Health Clinical Center (CC) | EARLY_Phase 1 |
| Completed | Trial With Taxotere and Cisplatin in Non-operable Adrenocortical Carcinoma NCT00324012 | Rigshospitalet, Denmark | Phase 2 |
| Active Not Recruiting | Preclinical Study Towards an Immunotherapy in Adrenocortical Carcinoma NCT00457587 | University of Wuerzburg | — |
| Recruiting | German Adrenocortical Carcinoma Registry NCT00453674 | University of Wuerzburg | — |
| Recruiting | Adrenal Tumors - Pathogenesis and Therapy NCT00669266 | University of Wuerzburg | — |
| Completed | Natural History Study of Infants With Adrenal Masses Found on Prenatal and/or Neonatal Imaging NCT00445718 | Children's Oncology Group | — |
| Completed | Combination Chemotherapy With Suramin Plus Doxorubicin in Treating Patients With Advanced Solid Tumors NCT00003038 | Mayo Clinic | Phase 1 |
| Terminated | S9427, Suramin in Treating Patients With Stage III or Stage IV Adrenocortical Cancer Incurable by Surgery NCT00002921 | SWOG Cancer Research Network | Phase 2 |
| Completed | Combination Chemotherapy and Tamoxifen in Treating Patients With Solid Tumors NCT00002608 | Ottawa Regional Cancer Centre | Phase 2 |