Trials / Completed
CompletedNCT03179631
Long-Term Outcomes of Ataluren in Duchenne Muscular Dystrophy
A Phase 3, Randomized, Double-blind, Placebo-controlled Efficacy and Safety Study of Ataluren in Patients With Nonsense Mutation Duchenne Muscular Dystrophy and Open-Label Extension
- Status
- Completed
- Phase
- Phase 3
- Study type
- Interventional
- Enrollment
- 360 (actual)
- Sponsor
- PTC Therapeutics · Industry
- Sex
- Male
- Age
- 5 Years
- Healthy volunteers
- Not accepted
Summary
This study is a long-term study of ataluren in participants with nonsense mutation Duchenne muscular dystrophy.
Detailed description
This study is a randomized, double-blind, placebo-controlled, 72-week study, followed by a 72-week open-label period. The purpose is to characterize the long-term effects of ataluren-mediated dystrophin restoration on disease progression. Participants will be randomized in a 1:1 ratio to ataluren or placebo. Participants will receive blinded study drug three times daily (TID) at morning, midday, and evening for 72 weeks, after which all participants will receive open-label ataluren for an additional 72 weeks (144 weeks in total). Study assessments will be performed at clinic visits every 12 weeks during the double-blind period and every 24 weeks during the open-label period.
Conditions
- Muscular Dystrophy, Duchenne
- Muscular Dystrophies
- Muscular Disorders, Atrophic
- Muscular Diseases
- Musculoskeletal Disease
- Neuromuscular Diseases
- Nervous System Diseases
- Genetic Diseases, X-Linked
- Genetic Diseases, Inborn
Interventions
| Type | Name | Description |
|---|---|---|
| DRUG | Ataluren | 10, 20 mg/kg |
| DRUG | PLACEBO | 10, 20 mg/kg |
Timeline
- Start date
- 2017-07-06
- Primary completion
- 2022-03-05
- Completion
- 2023-07-25
- First posted
- 2017-06-07
- Last updated
- 2026-03-10
- Results posted
- 2026-03-10
Locations
64 sites across 18 countries: United States, Australia, Brazil, Bulgaria, Canada, China, Hong Kong, India, Japan, Malaysia, Mexico, Poland, Puerto Rico, Russia, South Korea, Taiwan, Thailand, Turkey (Türkiye)
Regulatory
- FDA-regulated drug study
Source: ClinicalTrials.gov record NCT03179631. Inclusion in this directory is not an endorsement.