Clinical Trials Directory

Trials / Completed

CompletedNCT04270682

Study to Evaluate Patients With Cerebrotendinous Xanthomatosis (RESTORE)

A Phase 3 Study to Evaluate the Effects of Chenodeoxycholic Acid in Adult and Pediatric Patients With Cerebrotendinous Xanthomatosis

Status
Completed
Phase
Phase 3
Study type
Interventional
Enrollment
19 (actual)
Sponsor
Mirum Pharmaceuticals, Inc. · Industry
Sex
All
Age
1 Month
Healthy volunteers
Not accepted

Summary

The study is made up of two cohorts: a randomized double-blind crossover (placebo withdrawal with rescue) study among patients ≥ 16 years of age (adult cohort) and an open-label dose titration study among pediatric patients ≥1 month and \<16 years of age (pediatric cohort)

Conditions

Interventions

TypeNameDescription
DRUGBlinded CDCA 250 mg TIDAdult cohort patients will receive blinded 250 mg CDCA TID or placebo during the double-blind periods based upon their treatment assignment.
DRUGPlaceboAdult cohort patients will receive blinded 250 mg CDCA TID or placebo during the double-blind periods based upon their treatment assignment.
DRUGOpen-Label CDCA 250 mg TIDAdult cohort patients will receive open-label 250 mg CDCA TID during the run-in and washout periods of the study or as rescue medication during the double-blind periods, if needed, based on clinical symptoms.
DRUGRescue Medication CDCA 250 mg TIDCDCA 250 mg TID will be provided as rescue medication during the double-blind periods, if needed, based on laboratory results.
DRUGCDCA Weight-Based Dose TIDPatients in the pediatric cohort will complete a weight-based dose titration to a tolerated dose and will maintain that tolerated dose for the remainder of the study. Pediatric cohort dosing of CDCA will not exceed an equivalent dose of 750 mg/day.

Timeline

Start date
2020-01-31
Primary completion
2023-07-13
Completion
2023-10-04
First posted
2020-02-17
Last updated
2024-10-28
Results posted
2024-10-28

Locations

12 sites across 2 countries: United States, Brazil

Regulatory

Source: ClinicalTrials.gov record NCT04270682. Inclusion in this directory is not an endorsement.