Clinical Trials Directory

Trials / Completed

CompletedNCT02552628

WILSTIM - DBS (WILson STIMulation - Deep Brain Stimulation)

DEEP BRAIN STIMULATION FOR SEVERE DYSTONIA ASSOCIATED WITH WILSON'S DISEASE. A Prospective Multicenter Meta-analysis of Nof1 Trials

Status
Completed
Phase
N/A
Study type
Interventional
Enrollment
5 (actual)
Sponsor
Hospices Civils de Lyon · Academic / Other
Sex
All
Age
18 Years – 60 Years
Healthy volunteers
Not accepted

Summary

Dystonia in Wilson's disease represent a major issue. The persistence of disabling motor symptoms despite medical treatments justifies conducting a study on deep brain stimulation (DBS) in Wilson's disease (WD). For bradykinetic patients, subthalamic nucleus (STN) could be considered as a better target than the globus pallidus (GPi). For patients with hyperkinetic dystonia, the internal globus pallidus (GPi) will be chosen as the target of DBS. The investigators hypothesize that STN DBS will improve Wilson's disease patients, who, despite copper chelators drugs, are still impaired by severe dystonia and akinesia (more or less associated with other movement disorders). The investigators primary objective is to demonstrate the efficacy of STN/GPi DBS on dystonia associated with Wilson's disease. Secondary objectives: * To evaluate the impact of STN/GPi DBS on other movements disorders (tremor, Parkinsonism, chorea) observed in Wilson's disease. * To describe cognitive status of patients and to evaluate the consequences of STN/GPi DBS on cognition and behavioral aspects of the disease. * To evaluate the consequences of the stimulation on speech and swallowing. * To evaluate the social impact of STN/GPi DBS in Wilson's disease. * To evaluate the safety of STN/GPi DBS in the specific context of Wilson's disease.

Detailed description

4 periods of stimulation on and off, sequence randomized at Day 0.

Conditions

Interventions

TypeNameDescription
DEVICEMedtronic, Activa® PC "on"
DEVICEMedtronic, Activa® PC "off"

Timeline

Start date
2016-01-01
Primary completion
2022-07-20
Completion
2022-07-20
First posted
2015-09-17
Last updated
2025-08-22

Locations

3 sites across 1 country: France

Source: ClinicalTrials.gov record NCT02552628. Inclusion in this directory is not an endorsement.